HealthSearch

Health Guide
Images

Port-wine stain

Definition

A port-wine stain is a birthmark in which swollen blood vessels create a reddish-purplish discoloration of the skin.

Alternative Names

Nevus flammeus

Causes

Port-wine stains are caused by an abnormal formation of tiny blood vessels in the skin.

In rare cases, port-wine stains are a sign of Sturge-Weber syndrome or Klippel-Trenaunay-Weber syndrome.

Symptoms

Early-stage port-wine stains are usually flat and pink. As the child gets older, the stain grows with the child and the color may deepen to dark red or purple. Port-wine stains occur most often on the face, but can appear anywhere on the body. Over time, the area can become thickened and take on a cobblestone-like appearance.

Exams and Tests

The health care provider can usually diagnose a port-wine stain by looking at the skin.

In a few cases, a skin biopsy is needed. Depending on the location of the birthmark and other symptoms, the provider may want to do an intraocular pressure test or x-ray of the skull.

An MRI or CT scan of the brain may also be done.

Treatment

Many treatments have been tried for port-wine stains, including freezing, surgery, radiation, and tattooing.

Laser therapy is most successful in removing port-wine stains. It is the only method that can destroy the tiny blood vessels in the skin without causing much damage to the skin. The exact type of laser used depends on the person's age, skin type, and particular port-wine stain.

Outlook (Prognosis)

Stains on the face respond better to laser therapy than those on the arms, legs, or middle of the body. Older stains may be more difficult to treat.

Possible Complications

Complications may include:

  • Deformity and increasing disfigurement
  • Emotional and social problems related to their appearance
  • Development of glaucoma in people with port-wine stains involving upper and lower eyelids
  • Neurologic problems when port-wine stain is associated with a disorder such as Sturge-Weber syndrome

When to Contact a Medical Professional

All birthmarks should be evaluated by the provider during a routine examination.

References

Brightman LA,  Geronemus RG, Reddy KK. Laser treatment of port-wine stains. Clin Cosmet Investig Dermatol. 2015.12;8:27-33. PMID: 25624768 www.ncbi.nlm.nih.gov/pubmed/25624768.

Habif TP. Vascular tumors and malformations. In: Habif TP, ed. Clinical Dermatology. 6th ed. Philadelphia, PA: Elsevier; 2016:chap 23.

Martin KL. Vascular disorders. In: Kliegman RM, Stanton BF, St. Geme JW, Schor NF, eds. Nelson Textbook of Pediatrics. 20th ed. Philadelphia, PA: Elsevier Saunders; 2016:chap 650.


Review Date: 4/14/2017
Reviewed By: Kevin Berman, MD, PhD, Atlanta Center for Dermatologic Disease, Atlanta, GA. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. Editorial team.
The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Call 911 for all medical emergencies. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. © 1997- A.D.A.M., Inc. Any duplication or distribution of the information contained herein is strictly prohibited.